嗜铬细胞瘤是来源于神经嵴的产生儿茶酚胺的肿瘤。原发性心脏嗜铬细胞瘤是极为罕见的，全世界目前见于文献报道的仅为100例左右，北京协和医院心外科去年1月份成功进行了一例心脏嗜铬细胞瘤切除手术，患者为中年女性，肿瘤同时侵犯左右心房，其MIBG闪烁扫描的结果正常，但奥曲肽显像结果异常。肿瘤在体外循环下被成功切除。该病例报告已经发表在著名心胸外科专业杂志Annals of Thoracic Surgery上。

　　本文中的图表和表格：

　　Fig 1. (A) 99m-Technetium-labeled hydrazinonicotinyl-Tyr3-octretide scintiscan demonstrated a focus of intense uptake on right side of heart silhouette. (B) Contrast-enhanced computed tomographic scan illustrated tumor (arrow) overlying interatrial groove. (LA = left atrium; RA = right atrium.)

　　Fig 2. Coronary angiogram demonstrated a tumor blush with 2 feeding vessels (white arrows) branching from left circumflex artery.

　　Fig 3. Resected cardiac pheochromocytoma.

　　Primary Cardiac Pheochromocytoma Involving Both Right and Left Atria

　　Xingrong Liu, MD, Qi Miao, MD , Heng Zhang, MD, Chaoji Zhang, MD, Lihua Cao, MD, Guotao Ma, MD, Zhengpei Zeng, MD

　　Pheochromocytomas are catecholamine-producing paragangliomas derived from the neural crest. Primary cardiac pheochromocytoma is extremely rare. We describe a case of cardiac pheochromocytoma involving both right and left atria in a middle-aged woman. Metaiodobenzylguanidine (MIBG) scintiscan results were normal, but results from an octreotide scan were abnormal. The tumor was successfully resected using cardiopulmonary bypass (CPB).

对此病例的病因及治疗相关的讨论请进入爱爱医新利18手机

查看原文章请点击进入